Neurofisiologia delle malattie neurodegenerative

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Gruppo guidato da Filippo Tempia

Neurofisiologia delle malattie neurodegenerative

Pubblicazioni

2022

Claudia Cristiano, Eriola Hoxha, Pellegrino Lippiello, Ilaria Balbo, Roberto Russo, Filippo Tempia, Maria Concetta Miniaci (2022) Maternal treatment with sodium butyrate reduces the development of autism-like traits in mice offspring. Biomedicine & Pharmacotherapy 156: 113870. https://doi.org/10.1016/j.biopha.2022.113870

Balbo I, Montarolo F, Genovese F, Tempia F, Hoxha E. Effects of the administration of Elovl5-dependent fatty acids on a spino-cerebellar ataxia 38 mouse model Behav Brain Funct 18, 8 (2022). https://doi.org/10.1186/s12993-022-00194-4

Montarolo, Francesca; Martire, Serena; Francesco, Chiara; Allegra, Sarah; Silvia, De Francia; Hoxha, Eriola; Tempia, Filippo; Alfonso, Capobianco Marco; Bertolotto, Antonio (2022) NURR1 deficient mice have age- and sex-specific behavioral phenotypes. J Neurosci Res 100:1747-1754. https://doi.org/10.1002/jnr.25067

2021

Eriola Hoxha, Ilaria Balbo, Roberta Parolisi, Matteo Audano, Francesca Montarolo, Francesco Ravera, Michela Guglielmotto, Luisa Muratori, Stefania Raimondo, Eleonora Di Gregorio, Annalisa Buffo, Alfredo Brusco, Barbara Borroni, Nico Mitro, Donatella Caruso, Filippo Tempia (2021) Elovl5 is required for proper action potential conduction along peripheral myelinated fibers. Glia. 17 June 2021 https://doi.org/10.1002/glia.24048 

Ilaria Balbo, Francesca Montarolo, Enrica Boda, Filippo Tempia and Eriola Hoxha (2021) Elovl5 Expression in the Central Nervous System of the Adult Mouse. Front. Neuroanat., 29 April 2021 doi.org/10.3389/fnana.2021.669073

2020

Lippiello P, Hoxha E, Tempia F, Miniaci MC. (2020) GIRK1-mediated inwardly rectifying potassium current is a candidate mechanism behind Purkinje cell excitability, plasticity and neuromodulation. Cerebellum, Online First 02 July 2020. https://doi.org/10.1007/s12311-020-01158-y. Lippiello, Pellegrino; Hoxha, Eriola; Cristiano, Claudia; Malvicini, Emilia;

Stanley, Adrien; Russo, Roberto; Tempia, Filippo; Miniaci, Maria. (2020) Role of β3-adrenergic receptor in the modulation of synaptic transmission and plasticity in mouse cerebellar cortex. J Neuroscie Res 98: 2263-2274. https://doi.org/10.1002/jnr.24712.

2019

Mancini C, Hoxha E, Iommarini L, Brussino A, Richter U, Montarolo F, Cagnoli C, Parolisi R, Gondor Morosini DI, Nicolò V, Maltecca F, Muratori L, Ronchi G, Geuna S, Arnaboldi F, Donetti E, Giorgio E, Cavalieri S, Di Gregorio E, Pozzi E, Ferrero M, Riberi E, Casari G, Altruda F, Turco E, Gasparre G, Battersby BJ,Porcelli AM, Ferrero E, Brusco A, Tempia F. Mice harbouring a SCA28 patient mutation in AFG3L2 develop late-onset ataxia associated with enhanced mitochondrial proteotoxicity. Neurobiol Dis. 2019 Apr;124:14-28. doi: 10.1016/j.nbd.2018.10.018. Epub 2018 Oct 30. PubMed PMID: 30389403.

Hoxha E, Marcinnò A, Montarolo F, Masante L, Balbo I, Laezza F, Tempia F (2019) Emergingroles of Fgf14 in behavioral control. Behavioral Brain Research 356: 257-265.

Manes M, Alberici A, Di Gregorio E, Boccone L, Premi E, Mitro N, Pasolini MP,Pani C, Paghera B, Orsi L, Costanzi C, Ferrero M, Tempia F, Caruso D, Padovani A, Brusco A, Borroni B (2019) Long-termefficacy of Docosahexaenoic acid (DHA) for SpinocerebellarAtaxia 38 (SCA38) treatment: an open labelextension study. Parkinsonism & RelatedDisorders.

2018

Hoxha E, Lippiello P, Zurlo F, Balbo I, Santamaria R, Tempia F, Miniaci MC. The Emerging Role of Altered Cerebellar Synaptic Processing in Alzheimer's Disease. Front Aging Neurosci. 2018 Nov 27;10:396. eCollection 2018. Review.

Hoxha E, Balbo I, Miniaci MC, Tempia F (2018) Purkinje cell signaling deficits in animal models of ataxia. Front. Synaptic Neurosci. 10:6 (17 pages). eCollection 2018. Review. http://dx.doi.org/10.3389/fnsyn.2018.00006.

Cerrato V, Mercurio S, Leto K, Fucà E, Hoxha E, Bottes S, Pagin M, Milanese M, Ngan C-Y, Concina G, Ottolenghi S, Wei C-L, Bonanno G, Pavesi G, Tempia F, Buffo A, Nicolis SK (2018) Sox2 conditional mutation in mouse causes ataxic symptoms, cerebellar vermis hypoplasia, and postnatal defects of Bergmann glia. Glia. http://dx.doi.org/10.1002/glia.23448.

Eriola Hoxha*, Andrea Marcinnò*, Francesca Montarolo, Linda Masante, Ilaria Balbo, Fernanda Laezza, Filippo Tempia (2018) Emerging roles of Fgf14 in behavioral control. Behavioral Brain Research 356: 257-265. https://doi.org/10.1016/j.bbr.2018.08.034. 

Cecilia Mancini*, Eriola Hoxha*, Luisa Iommarini, Alessandro Brussino, Uwe Richter, Francesca Montarolo, Claudia Cagnoli, Roberta Parolisi, Diana Iulia Gondor Morosini, Valentina Nicolò, Francesca Maltecca, Luisa Muratori, Giulia Ronchi, Stefano Geuna, Francesca Arnaboldi, Elena Donetti, Elisa Giorgio, Simona Cavalieri, Eleonora Di Gregorio, Elisa Pozzi, Marta Ferrero, Evelise Riberi, Giorgio Casari, Fiorella Altruda, Emilia Turco, Giuseppe Gasparre, Brendan J. Battersby, Anna Maria Porcelli, Alfredo Brusco*, Filippo Tempia* (2018) Mice harbouring a SCA28 patient mutation in AFG3L2 develop late-onset ataxia associated with enhanced mitochondrial proteotoxicity. Neurobiol Dis. 2018 Oct 30. pii: S0969-9961(18)30320-6. doi: 10.1016/j.nbd.2018.10.018. *contributed equally

2017

Hoxha E, Gabriele RMC, Balbo I, Ravera F, Masante L, Zambelli V, Albergo C, Mitro N, Caruso D, Di Gregorio E, Brusco A, Borroni B, Tempia F. Motor Deficits and Cerebellar Atrophy in Elovl5 Knock Out Mice. Front Cell Neurosci. 2017 Oct 30;11:343. doi: 10.3389/fncel.2017.00343. eCollection 2017.

Hoxha E, Lippiello P, Scelfo B, Tempia F, Ghirardi M, Miniaci MC. (2017) Maturation and refinement of cerebellar cortical circuits in normal development and in murine models of autism. Neural Plasticity, Article ID 2017:6595740, 14 pages. Review. doi: 10.1155/2017/6595740.

Manes M, Alberici A, Di Gregorio E, Boccone L, Premi E, Mitro N, Pasolini MP, Pani C, Paghera B, Perani D, Orsi L, Costanzi C, Ferrero M, Zoppo A, Tempia F, Caruso D, Grassi M, Padovani A, Brusco A, Borroni B (2017) DHA is a beneficial replacement treatment for Spinocerebellar Ataxia 38 (SCA38). Ann Neurol. 2017 Oct 4. doi: 10.1002/ana.25059.

2016

Eriola Hoxha, Filippo Tempia, Pellegrino Lippiello, Maria Concetta Miniaci. (2016) Modulation, plasticity and pathophysiology of the parallel fiber-Purkinje cell synapse. Frontiers in Synaptic Neuroscience 8:35; doi: http://dx.doi.org/10.3389/fnsyn.2016.00035

Alshammari TK,Alshammari MA, Nenov MN, Hoxha E, Cambiaghi M, Marcinno A, James TF, Singh P, Labate D, Li J, Meltzer HY, Sacchetti B, Tempia F, Laezza F. Genetic deletion of fibroblast growth factor 14 recapitulates phenotypic alterations underlying cognitive impairment associated with schizophrenia. Transl Psychiatry (2016) 6, e806; http://dx.doi.org/10.1038/tp.2016.66

Barbara Borroni, Eleonora Di Gregorio, Laura Orsi, Giovanna Vaula, Chiara Costanzi, Filippo Tempia, Nico Mitro, Donatella Caruso, Marta Manes, Lorenzo Pinessi, Alessandro Padovani, Alfredo Brusco, Loredana Boccone (2016) Clinical and neuroradiological features of spinocerebellar ataxia 38 (SCA38). Parkinsonism & Related Disorders; http://dx.doi.org/10.1016/j.parkreldis.2016.04.030

Cupolillo D, Hoxha E, Faralli A, De Luca A, Tempia F, Rossi F, Carulli D (2016) Autistic-like traits and cerebellar dysfunction in Purkinje cell PTEN knock-out mice. Neuropsychopharmacol doi: 10.1038/npp.2015.339

Lippiello Pellegrino, Hoxha Eriola, Speranza Luisa, Volpicelli Floriana, Ferraro Angela, Leopoldo Marcello, Lacivita Enza, Perrone-Capano Carla, Tempia Filippo and Miniaci Maria Concetta. (2016) The 5-HT7 Receptor Triggers Cerebellar Long-Term Synaptic Depression via PKC-MAPK. J Neuropharmacol 101: 426-438. http://dx.doi.org/10.1016/j.neuropharm.2015.10.019

2015

Sadallah M, Labat-Gest V, Tempia F. Propagation of neuronal damage to embryonic grafts transplanted in the hippocampus of murine models of Alzheimer's disease. Rejuvination Res. (Instant Online ahead of print June 2, 2015) 

Tempia F, Hoxha E, Negro G, Alshammari MA, Alshammari TK, Panova-Elektronova N and Laezza F (2015) Parallel fiber to Purkinje cell synaptic impairment in a mouse model of spinocerebellar ataxia type 27. Front. Cell. Neurosci. 9:205. 

Sallam HS, Tumurbaatar B, Zhang WR, Tuvdendorj D, Chandalia M, Tempia F, Laezza F, Taglialatela G, Abate N. (2015) Peripheral adipose tissue insulin resistance alters lipid composition and function of hippocampal synapses. J Neurochem 133: 125-133.

Nenov MN, Tempia F, Denner L, Dineley KT, Laezza F. (2015) Impaired firing properties of dentate granule neurons in an Alzheimer's disease animal model are rescued by PPARγ agonism. J Neurophysiol 113: 1712-1726.

Lippiello P, Hoxha E, Volpicelli F, Lo Duca G, Tempia F*, Miniaci MC. (2015) Noradrenergic Modulation of the Parallel Fiber-Purkinje Cell Synapse in Mouse Cerebellum. Neuropharmacol 89: 33-42. DOI: 10.1016/j.neuropharm.2014.08.016. (* corresponding author)